Article: Disruption of cardio-pulmonary coupling in myopathies: Pathophysiological and mechanistic characterization with special emphasis on nemaline myopathy.
Frontiers in cardiovascular medicine
2022 Volume 9, Page(s) 996567
Abstract: The heart and lung are in continuous reciprocal interaction that creates a functional and anatomical reserve referred to as cardiopulmonary coupling (CPC). Disruption of CPC can occur due to various cardiac or pulmonary pathologies but also can occur in ... ...
Abstract | The heart and lung are in continuous reciprocal interaction that creates a functional and anatomical reserve referred to as cardiopulmonary coupling (CPC). Disruption of CPC can occur due to various cardiac or pulmonary pathologies but also can occur in patients with myopathies. Nemaline myopathy (NM) is a skeletal muscle heterogeneous disorder due to contractile proteins' gene mutations that impact lung and cardiac mechanics and thus is expected to adversely affect CPC in a complex manner. We present a case of NM and we review the literature on cardiac and pulmonary effects of myopathy-related disruption of CPC. |
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Language | English |
Publishing date | 2022-11-07 |
Publishing country | Switzerland |
Document type | Journal Article ; Review |
ZDB-ID | 2781496-8 |
ISSN | 2297-055X |
ISSN | 2297-055X |
DOI | 10.3389/fcvm.2022.996567 |
Database | MEDical Literature Analysis and Retrieval System OnLINE |
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