Article ; Online: Retroperitoneal yolk sac tumour encroaching the liver and adrenal gland with tumour thrombus in cavo-atrial region and hepatic veins.
BMJ case reports
2023 Volume 16, Issue 11
Abstract: Paediatric germ cell tumours (GCT) are rare tumours and are unique because of varied clinical presentation and locations. Yolk sac tumour is the predominant malignant histology and a serum marker; alpha fetoprotein is used to see treatment response and ... ...
| Abstract | Paediatric germ cell tumours (GCT) are rare tumours and are unique because of varied clinical presentation and locations. Yolk sac tumour is the predominant malignant histology and a serum marker; alpha fetoprotein is used to see treatment response and recurrent disease. It is extremely rare to find a retroperitoneal GCT with tumour thrombus extending up to the cavo-atrial region with involvement of the hepatic veins. We report a case of retroperitoneal yolk sac tumour (RPYST) with extension to the liver and right adrenal gland along with tumour thrombus in the inferior vena cava and in the right and middle hepatic veins. The child was operated after satisfactory response to chemotherapy. Excision of the tumour along with the right adrenal gland and around 5 cm of retro-hepatic caval resection was done. Inferior vena cava resection was tolerated without reconstruction. Currently child is disease-free and symptom-free at 22 months of follow-up with normal serum marker. |
|---|---|
| MeSH term(s) | Humans ; Child ; Hepatic Veins ; Endodermal Sinus Tumor/complications ; Endodermal Sinus Tumor/surgery ; Endodermal Sinus Tumor/pathology ; Atrial Fibrillation ; Thrombosis/etiology ; Thrombosis/surgery ; Thrombosis/pathology ; Vena Cava, Inferior/surgery ; Vena Cava, Inferior/pathology ; Liver/surgery ; Liver/pathology ; Adrenal Glands/diagnostic imaging ; Adrenal Glands/surgery ; Adrenal Glands/pathology ; Neoplasms, Germ Cell and Embryonal/pathology |
| Language | English |
| Publishing date | 2023-11-03 |
| Publishing country | England |
| Document type | Case Reports ; Journal Article |
| ISSN | 1757-790X |
| ISSN (online) | 1757-790X |
| DOI | 10.1136/bcr-2023-255968 |
| Database | MEDical Literature Analysis and Retrieval System OnLINE |
More links
Kategorien
Order via subito
This service is chargeable due to the Delivery terms set by subito. Orders including an article and supplementary material will be classified as separate orders. In these cases, fees will be demanded for each order.
Inter-library loan at ZB MED
Your chosen title can be delivered directly to ZB MED Cologne location if you are registered as a user at ZB MED Cologne.