Article ; Online: Primary cutaneous Rosai-Dorfman-Destombes disease with features mimicking IgG4-related disease: A challenging case report and literature review.
The Australasian journal of dermatology
2022 Volume 63, Issue 3, Page(s) 372–375
Abstract: Rosai-Dorfman-Destombes disease (RDD) is a rare histiocytic disorder affecting lymph nodes as well as extranodal sites. Although cutaneous involvement in RDD is common, primary cutaneous RDD is a distinct and not well-documented entity with unknown ... ...
Abstract | Rosai-Dorfman-Destombes disease (RDD) is a rare histiocytic disorder affecting lymph nodes as well as extranodal sites. Although cutaneous involvement in RDD is common, primary cutaneous RDD is a distinct and not well-documented entity with unknown aetiology and non-specific clinicopathological features. We report a case of a 57-year-old patient, who presented with an indolent skin nodule in the left sub-nipple area. Surgical excision was performed. Histological examination concluded to the diagnosis of cutaneous RDD with histological features mimicking IgG4-related disease. The diagnosis of systemic RDD with cutaneous involvement was ruled out after exclusion of extracutaneous involvement. No recurrence or systemic progression was observed during follow-up. The diagnosis of primary cutaneous RDD is very uncommon and hence is challenging for pathologist and dermatologist especially with features of IgG4-related disease. Careful systemic and microscopic examinations help in establishing the appropriate diagnosis. |
---|---|
MeSH term(s) | Histiocytosis, Sinus/pathology ; Humans ; Immunoglobulin G4-Related Disease/diagnosis ; Lymph Nodes/pathology ; Middle Aged ; Rare Diseases/pathology ; Skin Diseases/diagnosis ; Skin Diseases/pathology |
Language | English |
Publishing date | 2022-05-18 |
Publishing country | Australia |
Document type | Case Reports ; Journal Article ; Review |
ZDB-ID | 138052-7 |
ISSN | 1440-0960 ; 0004-8380 |
ISSN (online) | 1440-0960 |
ISSN | 0004-8380 |
DOI | 10.1111/ajd.13869 |
Database | MEDical Literature Analysis and Retrieval System OnLINE |
Full text online
More links
Kategorien
In stock of ZB MED Cologne/Königswinter
Zs.A 236: Show issues | Location: Je nach Verfügbarkeit (siehe Angabe bei Bestand) bis Jg. 1994: Bestellungen von Artikeln über das Online-Bestellformular Jg. 1995 - 2021: Lesesall (1.OG) ab Jg. 2022: Lesesaal (EG) |
Order via subito
This service is chargeable due to the Delivery terms set by subito. Orders including an article and supplementary material will be classified as separate orders. In these cases, fees will be demanded for each order.