Article ; Online: Subcutaneous Panniculitis-like T-cell Lymphoma with a HAVCR2 Mutation Diagnosed after 10 Years of Treatment with Glucocorticoids and Cyclosporine as Lupus Panniculitis.
Internal medicine (Tokyo, Japan)
2022 Volume 62, Issue 10, Page(s) 1537–1540
Abstract: Subcutaneous panniculitis-like T cell lymphoma (SPTCL) is a very rare cutaneous T cell lymphoma that has been reported to be associated with autoimmune disorders but is most commonly associated with systemic lupus erythematosus. We herein report a 26- ... ...
| Abstract | Subcutaneous panniculitis-like T cell lymphoma (SPTCL) is a very rare cutaneous T cell lymphoma that has been reported to be associated with autoimmune disorders but is most commonly associated with systemic lupus erythematosus. We herein report a 26-year-old man thought to have lupus panniculitis (LP) treated for 10 years with corticosteroids and cyclosporine. After several relapses with panniculitis, he was finally diagnosed with SPTCL, which was confirmed to have a HAVCR2 mutation for p.Tyr82Cys. We emphasize that rheumatologists should be aware of the possibility of SPTCL, despite its rare appearance, when making a diagnosis of LP or when encountering clinical manifestations that are not consistent with LP. |
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| MeSH term(s) | Male ; Humans ; Adult ; Panniculitis, Lupus Erythematosus/diagnosis ; Panniculitis, Lupus Erythematosus/pathology ; Glucocorticoids/therapeutic use ; Cyclosporine/therapeutic use ; Neoplasm Recurrence, Local/diagnosis ; Panniculitis/drug therapy ; Panniculitis/genetics ; Panniculitis/diagnosis ; Lymphoma, T-Cell/diagnosis ; Lymphoma, T-Cell/drug therapy ; Lymphoma, T-Cell/genetics ; Diagnosis, Differential ; Skin Neoplasms/diagnosis ; Mutation ; Hepatitis A Virus Cellular Receptor 2 | |||||
| Chemical Substances | Glucocorticoids ; Cyclosporine (83HN0GTJ6D) ; HAVCR2 protein, human ; Hepatitis A Virus Cellular Receptor 2 | |||||
| Language | English | |||||
| Publishing date | 2022-09-28 | |||||
| Publishing country | Japan | |||||
| Document type | Case Reports ; Journal Article | |||||
| ZDB-ID | 32371-8 | |||||
| ISSN | 1349-7235 ; 0021-5120 ; 0918-2918 | |||||
| ISSN (online) | 1349-7235 | |||||
| ISSN | 0021-5120 ; 0918-2918 | |||||
| DOI | 10.2169/internalmedicine.0428-22 | |||||
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| Database | MEDical Literature Analysis and Retrieval System OnLINE |
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