Article ; Online: Cronkhite-Canada syndrome with esophagus involvement and six-year follow-up: A case report.
World journal of gastroenterology
2024 Volume 30, Issue 8, Page(s) 984–990
Abstract: Background: Cronkhite-Canada syndrome (CCS) is a rare, noninherited disease characterized by gastrointestinal polyposis with diarrhea and ectodermal abnormalities. CCS polyps are distributed through the whole digestive tract, and they are common in the ... ...
Abstract | Background: Cronkhite-Canada syndrome (CCS) is a rare, noninherited disease characterized by gastrointestinal polyposis with diarrhea and ectodermal abnormalities. CCS polyps are distributed through the whole digestive tract, and they are common in the stomach and colon but very uncommon in the esophagus. Case summary: Here, we present a case of a 63-year-old man with skin hyperpigmentation accompanied by diarrhea, alopecia, and loss of his fingernails. Laboratory data indicated anemia, hypoalbuminemia, hypocalcemia, hypokalemia, and positive fecal occult blood. Endoscopy showed numerous polyps scattered throughout the digestive tract, including the esophagus. He was treated with nutritional support and glucocorticoids with remission of his symptoms. Conclusion: Comprehensive treatment led by hormonal therapy can result in partial or full remission of clinical symptoms. Treatment should be individualized for each patient according to their therapy response. Surveillance endoscopy is necessary for assessing mucosal disease activity and detecting malignant transformation. |
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MeSH term(s) | Male ; Humans ; Middle Aged ; Endoscopy, Gastrointestinal/adverse effects ; Glucocorticoids/therapeutic use ; Esophagus/pathology ; Intestinal Polyposis/complications ; Intestinal Polyposis/diagnosis ; Intestinal Polyposis/therapy ; Diarrhea/etiology |
Chemical Substances | Glucocorticoids |
Language | English |
Publishing date | 2024-03-14 |
Publishing country | United States |
Document type | Case Reports |
ZDB-ID | 2185929-2 |
ISSN | 2219-2840 ; 1007-9327 |
ISSN (online) | 2219-2840 |
ISSN | 1007-9327 |
DOI | 10.3748/wjg.v30.i8.984 |
Database | MEDical Literature Analysis and Retrieval System OnLINE |
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